Torsion of a wandering spleen in an adolescent with Gaucher disease.

نویسندگان

  • Şükrü Güngör
  • Mehmet Öztürk
  • Fatma İlknur Varol
  • Ahmet Sığırcı
  • Mukadder Ayşe Selimoğlu
چکیده

A wandering spleen is a rare condition characterized by the malposition of the spleen due to laxity or absence of its supporting ligaments. Although Gaucher disease generally presents with massive splenomegaly, which one of the predisposing causes of a wandering spleen, literature shows only one report of a wandering spleen in a child with Gaucher disease. In this case presentation, a 13-year-oldadolescent with Gaucher disease on enzyme replacement treatment was presented, who was detected having an abdominal mass on a routine visit and diagnosed with partial torsion of a wandering spleen associated with left lobe hypoplasia of the liver.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Splenic Torsion in a Wandering Spleen Presenting As Intestinal Obstruction

SUMMARY The -presented patient is a 4 year old boy who is a known case of Niemannpick disease. He presented with restlessness, anorexia, Vomiting and constipation. On the physical exam the cbdomen was distended and a large and a large and mobile mass in right lower quadrant was palpated. Plain abdominal X-Ray showed air-fluid levels. The patient underwent an emergent operation. The splenic ped...

متن کامل

Torsion chronique d'une rate baladeuse chez un adolescent: à propos d'un cas

Wandering or migrating spleen is a rare anomaly which is usually described in children. Complications, which include pedicle torsion, are common and can be life-threatening. We report the case of a 17 year-old patient with a long past medical history of epigastric pain suffering from wandering spleen with chronic torsion of the pedicle. The clinical picture was marked by spontaneously painful e...

متن کامل

Acute torsion of wandering spleen in a 17-year-old girl.

The acute torsion of wandering spleen is a very rare disease characterized by acute abdominal pain. Without early surgical intervention, wandering spleen can lead to splenic infarction or rupture. However, early clinical diagnosis is very difficult, so imaging modalities play an important role. We present a case of acute abdominal pain due to torsion of the wandering spleen in a 17-year-old gir...

متن کامل

Acute torsion of a wandering spleen.

The 'wandering spleen' is a rare condition due to extreme laxity or absence of ligaments that fix the organ in its normal anatomical position within the left upper quadrant. Without early surgical intervention, wandering spleen can lead to torsion and subsequent splenic infarction or rupture. Clinical suspicion plus urgent investigation and intervention are important, so as to salvage the splee...

متن کامل

Torsion of a wandering spleen: an unusual abdominal catastrophe.

Wandering spleen is a rare clinical entity characterised by splenic hypermobility resulting from laxity or maldevelopment of the suspensory gastrosplenic, splenorenal, and phrenicocolic ligaments. Diagnosis is quite difficult, especially in children because of the lack of symptoms and signs until splenic torsion have occurred. An array of investigations is possible but US with color Doppler, CT...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • The Turkish journal of gastroenterology : the official journal of Turkish Society of Gastroenterology

دوره 28 4  شماره 

صفحات  -

تاریخ انتشار 2017